VARIANT OF HERLYN WERNER WUNDERLICH SYNDROME – A RARE MULLERIAN DUCT ANAMOLY

Dr. K. Ramalingam, Dr. K. Sri Sowmya

Abstract


Introduction-The incidence of Mullerian duct anomalies is 0.5-5% , of which uterus didelphys/double uterus is rarest of
all anomalies. Knowledge on them is important as they have great impact on women's quality of life.
Case Report-A 15 year old unmarried girl admitted in the Departement of OBGY , NRI hospital,guntur with pain
abdomen of one month duration. Her cycles are regular with severe dysmenorrhoea. USG and MRI pelvis revealed Two
uterine horns with two endometrial cavities, two cervical canals with obstructed left horn with hematometra of size
16.5*5.5cm with hematotrachelos, hematosalphinx with absent left kidney. Laparotomy was done and drianage of
hematometra , excision of left sided cervix, uterine horn and the fallopian tube with fimbrial cyst was done.
Postoperatively, patient was relieved of her symptoms.
Discussion – Mullerian duct anomalies occur due to abnormal embryological development of Mullerian duct. They
often associated with renal anomalies. They present with amenorrhoea,severe dysmenorrhoea and palpable mass due
to underlying hematotrachelometra. Association of uterine didelphys with renal agenesis and obstructed hemi vagina is
called Herlyn-Werner-Wunderlich syndrome, and our case is variant of it.
Conclusion – Early and accurate diagnosis is vital because untreated cases may develop retrograde tubal reflux ,
endometriosis, impaired fertility and obstetric complications in later life


Keywords


Mullerian Duct anomalies, Uterus Didelphys, Hematometra

Full Text:

PDF

Refbacks

  • There are currently no refbacks.